Human frataxin (full length mature form, residues 56-210)
Conjugate
Unconjugated
Form
Liquid
Concentration
1 mg/ml
Purification
purified
Storage buffer
HEPES buffered saline
Preservative
0.02% sodium azide
Storage Conditions
4° C, do not freeze
Tested Applications
Dilution *
Immunocytochemistry (ICC)
0.5 ug/ml
Immunofluorescence (IF)
Assay Dependent
Western Blot (WB)
3-5 ug/ml
* Suggested working dilutions are given as a guide only. It is recommended that the user titrate the product for use in their own experiment using appropriate negative and positive controls.
Background/Target Information
FXN is a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA results in Friedreich ataxia.
原厂资料:
注意事项:
For Research Use Only. Not for use in diagnostic procedures.